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Showing 1 to 3 of 3 for “"amyotrophic lateral sclerosi"”.

  1. UPPER MOTOR NEURON BURDEN IN AMYOTROPHIC LATERAL SCLEROSIS: CLINICAL AND IMAGING FEATURES, AND THE ROLE OF IRON METABOLISM

    Introduzione. La Sclerosi Laterale Amiotrofica (SLA) è una patologia rara, a prognosi infausta, in cui la degenerazione del primo e del secondo motoneurone sono coinvolte in modo selettivo. Un elemento di difficoltà nella diagnosi e nel definire una terapia efficace è la considerevole …

    milano Repository record for UPPER MOTOR NEURON BURDEN IN AMYOTROPHIC LATERAL SCLEROSIS: CLINICAL AND IMAGING FEATURES, AND THE ROLE OF IRON METABOLISM (opens in a new tab)

  2. AGGREGATION MECHANISMS OF TDP-43 PROTEIN IN RESPONSE TO STRESS IN AMYOTROPHIC LATERAL SCLEROSIS AND THERAPEUTIC APPROACHES

    Amyotrophic Lateral Sclerosis (ALS) is a rare neurodegenerative disorder affecting upper and/or lower motor neurons for which no effective cure is available to date. The neuropathological hallmark of the disease, present in 97% of ALS cases, consists in TDP- 43 proteinopathy characterized by the …

    milano Repository record for AGGREGATION MECHANISMS OF TDP-43 PROTEIN IN RESPONSE TO STRESS IN AMYOTROPHIC LATERAL SCLEROSIS AND THERAPEUTIC APPROACHES (opens in a new tab)